20 products were found matching "K00253"!
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IVD Protein, Mouse, Recombinant (His)
Item number: TGM-TMPY-05066-100ug
Description: IVD (Isovaleryl-CoA Dehydrogenase) is a Protein Coding gene. IVD is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. IVD plays an essential role in processing proteins obtained from the diet. The body breaks down proteins from food into smaller parts called amino acids....
| Keywords: | AI463340, 6720455E18Rik, 1300016K07Rik, isovaleryl-CoA dehydrogenase |
| MW: | 45.3 kD |
699.00€
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Isovaleroylglycine
Item number: Cay17581-500
Isovaleroylglycine is a compound found in the urine of patients with isovaleric acidemia, a disorder created by defective leucine metabolism due to a deficiency in the isovaleryl coenzyme A dehydrogenase. It has been used as a diagnostic tool in the diagnosis of various acidemias and mitochondrial fatty acid...
| Keywords: | N-Isovalerylglycine, N-(3-methyl-1-oxobutyl)-glycine |
| CAS | 16284-60-9 |
| MW: | 159.2 D |
From 61.00€
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Anti-IVD
Item number: E-AB-65247.120
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript...
| Keywords: | Anti-IVD, EC=1.3.8.4, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, IVD Polyclonal Antibody |
| Application: | WB |
| Host: | Rabbit |
| Species reactivity: | human, mouse |
From 243.00€
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Isovaleryl-DL-carnitine-d3 (chloride)
Item number: Cay26573-1
Isovaleryl-DL-carnitine-d3 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine (Cay-21489, Cay-16749). Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of...
| Keywords: | DL-Isovalerylcarnitine-d3, 3-carboxy-N,N-dimethyl-N-(methyl-d3)-2-((3-methylbutanoyl)oxy)propan-1-aminium, monochloride |
| Application: | GC-MS, LC-MS, quantification, internal standard, isovaleryl-CoA dehydrogenase defiency marker |
| MW: | 278.7 D |
From 94.00€
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Anti-IVD
Item number: ARG58891.100
| Keywords: | Anti-IVD, EC=1.3.8.4, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Application: | WB |
| Host: | Rabbit |
| Species reactivity: | human, mouse |
658.00€
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Anti-IVD
Item number: E-AB-18718.120
IVD(Isovaleryl CoA dehydrogenase,mitochondrial) is a member of the acylCoA dehydrogenase family and is involved in the catabolism of leucine. In size,IVD precursor and mature proteins produced by class I mutants are indistinguishable from their normal counterparts. Class II,III,and IV mutants make IVD precursor...
| Keywords: | Anti-IVD, EC=1.3.8.4, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, IVD Polyclonal Antibody |
| Application: | WB, ELISA |
| Host: | Rabbit |
| Species reactivity: | human, mouse, rat |
From 89.00€
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Anti-IVD
Item number: ATA-HPA041391.100
Protein function: Catalyzes the conversion of isovaleryl-CoA/3-methylbutanoyl- CoA to 3-methylbut-2-enoyl-CoA as an intermediate step in the leucine (Leu) catabolic pathway (PubMed:7640268). To a lesser extent, is also able to catalyze the oxidation of other saturated short-chain acyl-CoA thioesters as...
| Keywords: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial |
| Application: | ICC, IHC, WB |
| Host: | Rabbit |
| Species reactivity: | human |
477.00€
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Isovaleryl-DL-carnitine-d9 (chloride)
Item number: Cay37213-1
Isovaleryl-DL-carnitine-d9 is intended for use as an internal standard for the quantification of isovaleryl-DL-carnitine by GC- or LC-MS. Isovaleryl-DL-carnitine is a derivative of carnitine (Cay-21489, Cay-16749). Increased levels of isovaleryl carnitine are associated with isovaleric acidemia, an inborn error of...
| Keywords: | DL-Isovalerylcarnitine-d9, 3-carboxy-N,N,N-tris(methyl-d3)-2-((3-methylbutanoyl)oxy)propan-1-aminium, monochloride |
| Application: | GC-MS, LC-MS internal standard, quantification, isovaleryl-CoA dehydrogenase defiency marker |
| CAS | 2608872-54-2 |
| MW: | 290.8 D |
From 150.00€
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NEW
IVD (human), recombinant protein
Item number: ABS-PP-1684.20
| Keywords: | Isovaleryl-CoA dehydrogenase, mitochondrial, IVD, Butyryl-CoA dehydrogenase, Recombinant Human IVD Protein |
| Expressed in: | E.coli |
| Origin: | human |
| MW: | 43.5 kD |
From 90.00€
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Anti-IVD
Item number: CSB-PA011921GA01HU.100
Host Species: Rabbit. Isotype: IgG. Buffer: PBS with 0.1% Sodium Azide, 50% Glycerol, pH 7.3. -20°C, Avoid freeze / thaw cycles. Storage: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Purification Method: Antigen Affinity Purified. Target Name: IVD. Antigen Species: Human
| Keywords: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, ACAD2 antibody, FLJ12715... |
| Application: | ELISA, IHC |
| Host: | Rabbit |
| Species reactivity: | human, mouse, rat |
552.00€
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Anti-IVD
Item number: CSB-PA011921LA01HU.100
Host Species: Rabbit. Isotype: IgG. Buffer: Preservative: 0.03% Proclin 300Constituents: 50% Glycerol, 0.01M PBS, pH 7.4. Storage: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Purification Method: >95%, Protein G purified. Target Name: IVD. Antigen Species: Human
| Keywords: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, ACAD2 antibody, FLJ12715... |
| Application: | ELISA, IHC |
| Host: | Rabbit |
| Species reactivity: | human |
From 167.00€
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Anti-IVD, FITC conjugated
Item number: CSB-PA011921LC01HU.100
Host Species: Rabbit. Isotype: IgG. Buffer: Preservative: 0.03% Proclin 300Constituents: 50% Glycerol, 0.01M PBS, pH 7.4. Storage: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze. Purification Method: >95%, Protein G purified. Target Name: IVD. Antigen Species: Human
| Keywords: | Anti-IVD, Anti-Butyryl-CoA dehydrogenase, Anti-Isovaleryl-CoA dehydrogenase, mitochondrial, ACAD2 antibody, FLJ12715... |
| Host: | Rabbit |
| Species reactivity: | human |
From 167.00€
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